Multifocal, recurrent malignant chondroid syringoma with visceral metastases: A case report and literature review

Ann Meredith Garcia, Jenny Maureen Atun, Gracieux Fernando


We present the unusual case of malignant chondroid syringoma (MCS) in a 64-year-old male with recurrent nodular skin lesions and visceral metastases. The patient underwent repeated excisions, with eventual development of widespread nodules and multiple pulmonary and hepatic nodules. Systemic chemotherapy was planned. MCS is a very rare skin adnexal tumor of the sweat glands with only around 50 cases reported worldwide. To the authors’ knowledge, this is the first reported case of MCS with a multifocal presentation and mucosal involvement.


Malignant Chondroid Syringoma, Malignant Mixed Tumor, Sweat Gland Carcinoma, Eccrine Carcinoma, Adnexal Carcinoma

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